A Case Report of Bochdalek Hernia with Anomalous Hepatic Lobe Heterotopia

Background: The most common type of Congenital Diaphragmatic Hernia (CDH) is Bochdalek hernia, which results from a postero-lateral diaphragmatic defect. Hepatic heterotopia is rare in CDH, and hepatic herniation has the worst prognosis.

Case Presentation: A neonate with right Bochdalek hernia (BH) and anomalous hepatic lobe heterotopia is presented. Intraoperatively, it was discovered that mal-rotated loops were herniating in the right hemithorax. After performing Ladd's procedure, the mal-rotated loops were reduced back into the abdomen, and the diaphragmatic defect was repaired over the anomalous liver lobe. Baby was discharged on 7th Postoperative day and follow ups showed good recovery.

Conclusion: This case report discusses the presentation, classification, and significance of this association. Our case report is noteworthy as Bochdalek hernia is very rarely associated with anomalous hepatic lobe and we believe that highlighting this association can benefit our pediatric surgery community in scientific research and clinical side.